Giant Retroperitoneal Tumor: An Unusual Localization of Malignant Peripheral Nerve Sheet Tumor
Journal Title: Scholars Journal of Medical Case Reports - Year 2018, Vol 6, Issue 10
Abstract
Malignant peripheral nerve sheath tumors (MPNST) are considered a rare entity, especially in the retro peritoneum. We report the case of a 32 years old woman, with the history of Von Recklinghausen disease, who presented a MNPST of 14,5 cm of diameter at the retroperitoneal cavity. There was no specific clinical symptom besides an abdominal swelling. The MRI showed a heterogeneous retroperitoneal mass that represses without invading the adjacent structures. We’ve conducted a mass resection without any adjuvant radio or chemotherapy. No sign of local recurrence was detected after one year follow up.
Authors and Affiliations
Taous H, Zahdi O, Hormat-Allah M, Bakkali T, Sefiani Y
Keywords
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