A case of Atypical Hemolytic Uremic Syndrome
Journal Title: Scholars Journal of Medical Case Reports - Year 2016, Vol 4, Issue 7
Abstract
Atypical hemolytic uremic syndrome (aHUS) is an extremely rare, life-threatening, progressive disease that frequently has a genetic component. In most cases, it is caused by chronic, uncontrolled activation of the complement system, a part of the body’s immune system that destroys and removes foreign particles. About 33-40% of patients die or develop end-stage renal disease (ESRD) with the first clinical episode of aHUS even with the best supportive care. We report a case of atypical HUSwith classical clinical & laboratory characteristics. Keywords:Acute kidney injury, complement, thrombotic microangiopathy.
Authors and Affiliations
Dr. Manisha Garg, Dr. Rajesh Kumar, Dr. Priyanshu Mathur, Dr. Vikas Gupta
Keywords
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