A Case report of a kid with Fibrodysplasia ossificans progressiva (FOP) and literature review for management of FOP
Journal Title: Journal of Pakistan Orthopaedic Association - Year 2023, Vol 35, Issue 01
Abstract
Fibrodysplasia ossificans progressiva is a connective tissue disorder in which connective tissues (ligaments, tendons) are gradually ossified and replaced by bone, there is extra skeletal bone formation. Any trauma can aggravate ossification in soft tissue. This condition usually is noticed at childhood. There is restriction of movements in major joints. We report a case of 2 years old boy with fibrodysplasia ossificans progressiva, who was brought by his parents to our OPD with history of swelling on back, scapular region and forehead for last 4 months. Parents also reported limitations of movements in spine and bilateral shoulders. Radiographs shows heterotrophic ossification in paraspinal muscles of dorsolumbar spine, and latissimus dorsi and trapezius muscle. Clinical and radiological evidence was of Fibrodysplasia ossificans progressiva. Treatment strategy is mainly based on prevention of trauma or injury, educating parents about the disease and medical management for acute painful episodes.
Authors and Affiliations
Hussain Wahab1, Asfandyar Khan2, Muhammad Ibrahim3, Raja Irfan Qadir4
Keywords
Related Articles
- EP ID EP740926
- DOI -
- Views 19
- Downloads 0
A subjective comparative analysis of quality of Short Answer Questions(SAQ) Items between Orthopedics and Other specialties used in internal examinations in MBBS course in Medical College of Lahore
ABSTRACT Objective: To compare the subjective quality of various items used in short answer questions (SAQ) papers between Orthopaedics and other specialties used in internal examinations in MBBS course in a Medical Col...
Organization of Disaster Relief Team for Earthquake Victims
To organize disaster relief teams in every medical non medical institution irrespective of fields, government, non-government like scouts, civil defence and NCC. Design Duration: Experience of team orthopaedics unit â...
Is Peroneus Longus autograft a safe and effective alternative for Anterior Cruciate Ligament Reconstruction?
Objective: To determine the functional outcomes Peroneus Longus (PL) autograft for Anterior Cruciate Ligament Reconstruction (ACLR). Methods: This descriptive study was conducted in AO Hospital Karachi Pakistan from 2...
Indications and Complications of Implant Removal from Extremities in Adult Orthopaedic Patients – A Retrospective Study in a Tertiary Care Hospital.
Objectives: To determine the indications and complications of implant removal from extremities in adult Orthopaedic patients in Abbasi Shaheed Hospital Karachi. Methods: This retrospective Cohort study was conducted i...
Pycnodysostosis: A Rare disorder
Pyknodysostosis is a rare autosomal recessive disorder characterized by the post natal onset of short limbs, short stature, and generalized hyperostosis along with acro-osteolysis with sclerosis of the terminal phalanges...