A Hematopathology Case Study of Familial Hemophagocytic Lymphohistiocytosis (HLH)

Abstract

Hemophagocytic lymphohistiocytosis is a rare hematologic disorder caused by dysregulated immune activation and carries a high rate of mortality. It is categorized broadly into Primary (Familial ) and secondary types. The recent classification of histiocytoses by Histiocytic society has placed Hemophagocytic lymphohistiocytosis in the “H” group. Greater awareness of Familial hemophagocytic lymphohistiocytosis is required among clinicians and pathologists for early diagnosis and a better survival. Here we report a case of Familial hemophagocytic lymphohistiocytosis correlating with clinical history, family history, bone marrow findings and genetic tests.

Authors and Affiliations

Dr. Anjaly S S, Dr. Siyad, Dr. Lila Rani Vijayaraghavan

Keywords

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  • EP ID EP714074
  • DOI 10.47191/ijmscrs/v2-i5-03
  • Views 23
  • Downloads 0

How To Cite

Dr. Anjaly S S, Dr. Siyad, Dr. Lila Rani Vijayaraghavan (2022). A Hematopathology Case Study of Familial Hemophagocytic Lymphohistiocytosis (HLH). International Journal Of Medical Science And Clinical Research Studies, 2(05), -. https://europub.co.uk/articles/-A-714074