A rare cutaneous tumor: Dermatofibrosarcoma protuberans

Journal Title: Nasza Dermatologia Online - Year 2017, Vol 8, Issue 4

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare indolent cutaneous tumor which has been considered as a low-grade dermal and subcutaneous fibrohistiocytic neoplasm. DFSP expands slowly but recurs frequently leading to the general assumption that DFSP is a locally aggressive neoplasm. This low-grade/borderline tumor which is generally found on trunk and proximal extremities of adults has limited potential for metastasis. Clinical presentation is usually typical with a red-brown or skin coloured indurated plaque with multiple nodules or protuberances. Histopathology of DFSP is also characteristical which demonstrates storiform pattern of uniform spindle cells infiltrating deep into the subcutaneous fat tissue constituting honeycomb appearence. Here, we report a case of DFSP in a 50-year-old woman who presents with a twenty year history of slowly growing mass on her left femoral area.

Authors and Affiliations

Nuran Alli

Keywords

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  • EP ID EP286272
  • DOI 10.7241/ourd.20174.126
  • Views 65
  • Downloads 0

How To Cite

Nuran Alli (2017). A rare cutaneous tumor: Dermatofibrosarcoma protuberans. Nasza Dermatologia Online, 8(4), 446-448. https://europub.co.uk/articles/-A-286272