A Unique Case of Maffucci’s Syndrome Presenting with Right Iliac Bone Chondrosarcoma
Journal Title: Scholars Journal of Medical Case Reports - Year 2016, Vol 4, Issue 10
Abstract
Abstract:We report a rare case of Maffucci’s syndrome in a 40 year old male patient presenting with dedifferentiated chondrosarcoma of right iliac bone developing from previous enchondroma along with multifocal enchondromas and haemangiomas involving various other bones predominantly on right side. In this case X-rays, CT scan and MRI were used to reach the final diagnosis. MRI was of aid to diagnose the dedifferentiated carcinoma even before the surgery. T2WI were used to distinguish between the dedifferentiated and the cartilaginous tumor. Furthermore, the dedifferentiated tumor had three elements-malignant fibrous histiocytoma, osteosarcoma and fibrosarcoma. This histological heterogeneity may be attributed to mesodermal dysplasia of Maffucci’s syndrome. Keywords:Maffucci’s syndrome, chondrosarcoma, enchondroma, right iliac bone.
Authors and Affiliations
Malpani Divya, Taori Abhijeet, Pasari Nikhilesh, Khandelwal Garima, Ajmera Arpita
Keywords
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