Adult Rasmussen's Encephalitis
Journal Title: Clinical Medical Reviews and Case Reports - Year 2016, Vol 3, Issue 12
Abstract
Rasmussen's Encephalitis (RE) is defined by the presence of partial seizures associated to focal progressive cortical atrophy and in advanced stages hemiparesis, hemianopia and cognitive impairment, though it may appear focal neurological deficits at onset; and it's more prevalent in childhood. Approximately, 10% presents at adulthood. Because of its immunologic physiopathology, RE is considered autoimmune epilepsy. Treatment is focused on antiepileptic drugs (AEDs), steroids, intravenous immunoglobulins (IVIg) and immunosuppressant drugs.
Authors and Affiliations
Keywords
Related Articles
- EP ID EP272209
- DOI 10.23937/2378-3656/1410144
- Views 136
- Downloads 0
Claudication: A Teachable Moment or Missed Opportunity!
Claudication is a common manifestation of Peripheral Arterial Disease (PAD) and atherosclerosis. Patients with claudication are at increased risk of cardiovascular events and limb-related complications. Optimal medical t...
Significance of Antiphospholipid Antibodies in Essential Cryoglobulinemia: A Case Report and Review of Literature
Cryoglobulinemia is a rare immune-complex-mediated small vessel vasculitis that has a smoldering clinical course and can potentially involve multiple organ systems. The discovery of its relationship with hepatitis C infe...
The Biliary Sinus: A Rare Late-Stage Complication of Cholecystectomy
A 53-year-old female patient who had undergone open cholecystectomy due to cholelithiasis 6 years earlier was admitted to hepatobiliary surgery unit with a painful mass in the right upper quadrant and fever. Ultrasonogra...
Bilateral Clavicle Fracture: A Rare Presentation of a Common Form of Orthopedic Birth Injury
A female newborn presented at day-1 with isolated right clavicle crepitus after vaginal delivery by certified nurse midwives. Shoulder dystocia was suspected at birth but delivery was successful with the sole aid of supr...
Unresolved Issues concerning Inadequate Immune Response after Rabies Post-Exposure Prophylaxis in an Immunocompromised Patient
We present an immunocompromised patient with inadequate immune response to the rabies post exposure prophylaxis (PEP), and our management strategy after this inadequate response. Currently, evidence based strategy for ac...