An Unusual Presentation of Motor Neuron Disease with Overlapping Features of both FTD-ALS and Madras Motor Neuron Disease
Journal Title: International Journal of Research and Review - Year 2018, Vol 5, Issue 6
Abstract
Madras motor neuron disease (MMND) presents in the young in the first two decades. The majority of the cases reported are from South India. The hallmark of MMND is sensorineural deafness (hearing loss due to nerve defect), atrophy and weakness of the limb muscles, cranial nerve palsies involving cranial nerves VII, IX and XII, facial and bulbar muscles (kind of muscles that control the chewing, swallowing and speech). MMND variant has the additional features of optic atrophy and cerebellar signs. It is a slowly progressive disease. We report a case of motor neuron disease with sensorineural deafness like Madras motor neuron disease variety but with relatively late presentation and rapid progression and associated with frontotemporaldementia-like FTD –ALS variant. So it’s a very rare case associated with some features of MMND and some features of FTD-ALS.
Authors and Affiliations
Dr Rajalaxmi Satapathy
Keywords
Related Articles
- EP ID EP480748
- DOI -
- Views 81
- Downloads 0
A Descriptive Study to Assess the Knowledge on Pregnancy Induced Hypertension among Antenatal Mothers Attending OG OPD at VMMCH, Karaikal
A study was conducted to assess the knowledge on Pregnancy Induced Hypertension among antenatal mothers attending OG OPD at VMMCH, Karaikal”. The objectives are to assess the knowledge on PIH among antenatal mothers and...
Impact of Self Concept and Emotional Intelligence on Adjustment of Adults
The purpose of the study is to determine the impact of self concept and emotional intelligence on adjustment of adults. A sample of three hundred post graduate students (one hundred fifty male and one hundred fifty femal...
GGE Biplot Analysis of Yield Stability in Multi -Season Trials of Early Matured Rice (O. Sativa) Genotypes in Rain Fed Lowland Ecosystem
The study was conducted in western part of Ethiopia at Assosa with the objective to identify better performance and stable rice genotypes under rainfed lowland rice ecosystem. Eighteen early matured rice genotypes were t...
Substance Abuse among the Undergraduate Students of a Medical College of Kolkata
Background- Drug dependence has been showing a rising trend all over the world perhaps as a result of newer and greater stresses related to rapid changes in life styles. During adolescence students are more vulnerable du...
Prevalence of Thyroid Dysfunction in Pregnancy and Its Outcome: The Indian Scenario
Thyroid gland is the most important endocrinal gland in the human’s body. It plays the important role in maintaining the metabolic rate and body’s homeostasis mechanism. [12] But however some physiological changes occur...