ANAESTHESIA FOR HERNIOTOMY IN PAEDIATRIC PATIENT WITH EHLERS-DANLOS SYNDROME: A Case Report
Journal Title: Journal of Indira Gandhi Institute of Medical Sciences - Year 2015, Vol 1, Issue 2
Abstract
Ehlers-Danlos syndrome (EDS) comprises a group of clinically and genetically heterogeneous heritable connective tissue disorders, chiefly characterized by joint hypermobility and instability, skin texture anomalies, and vascular and soft tissue fragility. As many tissues can be involved, the underlying molecular defect can manifest itself in many organs and with varying degrees of severity, with widespread implications for anaesthesia and perioperative management. In this case report we have focused on issues for anaesthesia for elective herniotomy & mesh hernioplasty in a 2 years old male child with clinical symptoms of classic type EDS. We searched various literatures and as per recommendation we have conducted this case under GA with laryngeal mask airway safely.
Authors and Affiliations
Vinod Kumar Verma, Vinit Thakur, Mumtaz Hussain, Nida Nawaz
ANAESTHESIA FOR HERNIOTOMY IN PAEDIATRIC PATIENT WITH EHLERS-DANLOS SYNDROME: A Case Report
Ehlers-Danlos syndrome (EDS) comprises a group of clinically and genetically heterogeneous heritable connective tissue disorders, chiefly characterized by joint hypermobility and instability, skin texture anomalies, and...
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