Anesthesia Management in Robinow Syndrome (A Case Report)
Journal Title: Bagcilar Medical Bulletin - Year 2017, Vol 2, Issue 1
Abstract
Robinow Syndrome (RS) is a rare disease characterized by anomalies in the face, head, external reproductive organs, and spine segmentation. The three main symptoms of the syndrome are fetal face appearance, genital hypoplasia, and gingival hyperplasia. Fifteen percent of the cases have congenital heart defects. Short neck, large tongue, and airway problems due to a structural disorder of the face may be observed. In this paper, we present our anesthesia practice in a case that had been diagnosed with RS.
Authors and Affiliations
Hacer Yeter, Murat Bagci, Aydin Firincioglu, Sitki Nadir Sinikoglu, Kerem Erkalp, Aysin Selcan
Keywords
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- EP ID EP50395
- DOI 10.5350/BMB20170306094925
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