Anesthetic Management of a Child with Tuberous Sclerosis Posted for Ventriculo-Peritoneal Shunt – A Case Report
Journal Title: GUJARAT CANCER SOCIETY RESEARCH JOURNAL - Year 2016, Vol 18, Issue 2
Abstract
Tuberous sclerosis is autosomal dominant condition that affects multiple system and causes benign tumor to grow in brain, kidneys, heart, eyes, lungs and skin. A combination of symptoms may include seizures, intellectual disability, developmental delay, behaviour abnormalities and problems in skin, abdomen, lung and kidneys. It has a classical triad of symptoms including epilepsy, skin lesions and mental retardation. An eight year old male pediatric patient was admitted in neurooncology department with complains of headache, drowsiness, vomiting, convulsion with Glassgow Coma Scale 8. He was diagnosed as having tuberous sclerosis with giant cell astrocytoma causing obstructive hydrocephalus. He was posted for ventriculoperitoneal shunt to relieve obstruction. The patient had several components from tuberous sclerosis including cardiac rhabdomyoma, skin lesion, hypertension, brain astrocytoma. Providing anesthesia in such patients is very challenging.
Authors and Affiliations
Amita Jansari, Priti Sanghvi, Nileshgiri Gauswami, Bipin Patel
Keywords
Related Articles
- EP ID EP197311
- DOI -
- Views 58
- Downloads 0
Burden of Infections in ICU: Strategies to Control
Patients are admitted in Intensive Care Unit (ICU) for close monitoring and constant medical care with life threatening illness. This is a study analysis is to know the rates of infections occurring in patients admitted...
Hospice Care is Not Only for Maggoted wound care!
Hospice care is a philosophy of caring that supports those nearing the end of life and in need of refuge. It is a system of caring specially designed to restore dignity and provide a sense of personal fulfillment to the...
Diagnosis of Thymolipoma with Fine Needle Aspiration Cytology: A Case Report
Thymolipomas are rare anterior mediastinal tumours composed of mature adipose tissue and benign thymic tissue arising from thymus gland. Fine needle aspiration cytology (FNAC) is now considered to be the diagnostic metho...
Malignant Mixed Mullerian Tumour of the Ovary- A Diagnostic Dilemma
Malignant mixed Mullerian tumour (MMMT) of ovary or ovarian carcinosarcoma is an aggressive neoplasm of postmenopausal females. Histologically, it is comprised of both epithelial and sarcomatous components. Prognosis is...
Febrile Neutropenia in Hematological Malignancies: Clinical and Microbiological Profile and Outcome
Febrile neutropenia (FN) is considered a medical emergency. Patients with hematological malignancies (HM) commonly experience FN. Broad spectrum antibiotics have to be started empirically to prevent complications. This s...