Anesthetic Management of a Child with Tuberous Sclerosis Posted for Ventriculo-Peritoneal Shunt – A Case Report
Journal Title: GUJARAT CANCER SOCIETY RESEARCH JOURNAL - Year 2016, Vol 18, Issue 2
Abstract
Tuberous sclerosis is autosomal dominant condition that affects multiple system and causes benign tumor to grow in brain, kidneys, heart, eyes, lungs and skin. A combination of symptoms may include seizures, intellectual disability, developmental delay, behaviour abnormalities and problems in skin, abdomen, lung and kidneys. It has a classical triad of symptoms including epilepsy, skin lesions and mental retardation. An eight year old male pediatric patient was admitted in neurooncology department with complains of headache, drowsiness, vomiting, convulsion with Glassgow Coma Scale 8. He was diagnosed as having tuberous sclerosis with giant cell astrocytoma causing obstructive hydrocephalus. He was posted for ventriculoperitoneal shunt to relieve obstruction. The patient had several components from tuberous sclerosis including cardiac rhabdomyoma, skin lesion, hypertension, brain astrocytoma. Providing anesthesia in such patients is very challenging.
Authors and Affiliations
Amita Jansari, Priti Sanghvi, Nileshgiri Gauswami, Bipin Patel
Keywords
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