Autoinflammatory Syndromes in the Practice of Pediatrician
Journal Title: Здоров`я дитини - Year 2014, Vol 5, Issue 56
Abstract
This review article provides information, characterization, identification and classification of diseases that have been attributed to a separate nosological group and called autoinflammatory diseases or syndromes (ABC). ABC concept was formed in the late 1990s; study and data accumulation are still actively pursued at the moment, and for this purpose there has been created international ABC register as a part of EUROFEVER program. Brief characteristics of both individual groups of diseases with typical genetic mutations and some clinical entities are provided. Drugs with proven therapeutic efficacy, including NSAIDs, GCs and genetically engineered biological agents, are listed.
Authors and Affiliations
S. N. Nedelskaya, I. A. Zhilenko, A. S. Merezhko, A. V. Shapran
Keywords
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