Bilateral hip and knee replacement in ochronotic (Alkaptonuria) arthropathy: Tips, tricks & precautions
Journal Title: International Journal of Orthopaedics Sciences - Year 2018, Vol 4, Issue 2
Abstract
Case: Alkaptonuria is a disorder of tyrosine metabolism having excretion of homogentisic acid in urine which gets dark when exposed to air. The disease is expressed as ochronosis of connective tissue with the significant involvement of large joints and spine. We present a case of a 56-year-old male having arthritis secondary to ochronosis of all large joints and bluish black discoloration of the bilateral sclera, skin of palm & earlobes. During surgery, black discoloration of cartilage, menisci, joint capsule, and tendons was revealed in bilateral hip and knee replacement. Conclusion: Due to stiffness of tissue encountered during surgical and anaesthetic procedure, this case serves as a learning high point for procedural modifications and surgical pearls which ensure a smooth management of the patient.
Authors and Affiliations
Dr. Sachin Awasthi, Dr. Chandrasekhar Verma, Dr. Swagat Mahapatra, Dr. Pankaj Aggarwal, Dr. SS Tripathy, Dr. Rajiv Ratan Singh Yadav
Keywords
Related Articles
- EP ID EP487069
- DOI 10.22271/ortho.2018.v4.i2l.112
- Views 124
- Downloads 0
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