Bilateral pleuropulmonary blastoma (PPB) in a 2- year-old girl: A case report with review of literature
Journal Title: Journal of Medical and Allied Sciences - Year 2017, Vol 7, Issue 1
Abstract
Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood accounting for 0.25-0.5% of primary lung tumors. PPB is a dysontogenic tumor composed of immature malignant epithelial and/or mesenchymal tissues whose features may resemble early embryological lung tissues. It is the pulmonary analog of other tumors of childhood including Wilms' tumor, neuroblastoma, hepatoblastoma, pancreatoblastoma and retinoblastoma. Morphologically, PPB has three types (I, II, and III). A fourth type (Ir) was added in 2006 by PPB registry. Type II and III are very aggressive malignancies with metastatic potential. Bilateral PPB is very rare. To the best of our knowledge, only two cases of bilateral PPB have been reported. No cases of bilateral PPB have been reported from India. Herein, we are reporting a case of bilateral PPB (type II) in a 2-year-old girl who presented with cough, dyspnea and mild fever for past 4 months. She died few days after admission.
Authors and Affiliations
Pradosh Kumar Sarangi| Department of Radiodiagnosis, S. C. B. Medical College & Hospital, Manglabag, Cuttack-753007, Odisha, India, H. S. Sagar| Department of Radiodiagnosis, S. C. B. Medical College & Hospital, Manglabag, Cuttack-753007, Odisha, India, Sanjay Kumar Nahak| Department of Radiodiagnosis, S. C. B. Medical College & Hospital, Manglabag, Cuttack-753007, Odisha, India, Jayashree Mohanty| Department of Radiodiagnosis, S. C. B. Medical College & Hospital, Manglabag, Cuttack-753007, Odisha, India, Sasmita Parida| Department of Radiodiagnosis, S. C. B. Medical College & Hospital, Manglabag, Cuttack-753007, Odisha, India
Keywords
Related Articles
- EP ID EP12767
- DOI 10.5455/jmas.252500
- Views 373
- Downloads 23
Management of culture-negative surgical site infections
Infections at the surgical site delays wound healing, prolongs hospitalization, increases morbidity and the overall costs. These issues are compounded when the postoperative infection is culturenegative. This article ou...
Pattern of dyslipidemia in ischemic stroke
The study aimed to assess dyslipidemia pattern including role of non HDL cholesterol (non HDLc) in ischemic strokes. A retrospective descriptive was conducted on 80 patients who were admitted to Osmania General Hospita...
Homology modeling and ligand interaction of human trafficking protein particle complex subunit 3-like protein and its correlation with Alzheimer’s disease
In order to understand the mechanism of molecular interactions at active sites of trafficking protein particle complex (TRAPPC) subunit 3-like protein (Accession number Q5T215) homology modeling and docking studies we...
Evaluation of antiulcer activity of Boswellia serrata bark extracts using aspirin induced ulcer model in albino rats
The effect of bark extracts of Boswellia serrata (Family Burseraceae) was evaluated in aspirin induced ulceration (200mg/kg) in albino rats. Antiulcer activity was evaluated by measuring ulcer index and percentage of u...
Assessment of postgraduate international students’ learning preferences at Tehran University of Medical Sciences, Tehran, Iran
Knowledge of learning preference can help to improve learning and teaching process and understand its implications. The aim of this study was to assess the preference for taking in and putting out information in learni...