Case Report – Mri Findings In Hirayama Disease Hirayama Disease----A Case Report
Journal Title: IOSR Journal of Dental and Medical Sciences (IOSR-JDMS) - Year 2017, Vol 16, Issue 12
Abstract
We report the MR findings in a case of Hirayama disease, a kind of cervical myelopathy related to flexion movements of the neck. In flexion MR studies, we can see the striking and pathognomonic picture of anterior shifting of posterior dura at the lower cervical spinal canal. In nonflexion studies, we find that asymmetric cord atrophy, especially at the lower cervical cord, though subtle, is highly suggestive of Hirayama disease. When it is seen, a flexion MR study is warranted to prove this diagnosis. Hirayama disease, also termed nonprogressive juvenile spinal muscular atrophy of the distal upper limbs, is a kind of cervical myelopathy related to flexion movements of the neck (1–6). The pathogenetic mechanism of this disease is attributed to forward displacement of the posterior wall of the lower cervical dural canal when the neck is in flexion, which causes marked, often asymmetric, flattening of the lower cervical cord (1, 6–9). We report a case of Hirayama disease and describe the pathognomonic findings at flexion magnetic resonance (MR) imaging. We also discuss the mechanism behind this characteristic appearance and describe findings suggestive of Hirayama disease on routine nonflexion MR studies.
Authors and Affiliations
Dr. Suman Chaudhary, Dr. Ravindra Kumar, Dr. A. P. Verma, Dr. Hemant
Keywords
Related Articles
- EP ID EP250431
- DOI 10.9790/0853-1010104
- Views 100
- Downloads 0
Cutaneous Horn Over Volar Aspect of Little Finger In A Female- A Case Report Running title Cutaneous Horn Over Volar Aspect of Little Finger In A Female
Cutaneous horns are uncommon protruding lesions from the skin which look like an Animal horn in a small form. They are usually found in sun exposed areas of the body, though cases have been reported of their occurrence i...
A study of the pattern of urinary sodium excretion in patients of essential hypertension versus normotensives A hospital based cross sectional study.
Introduction: One of the major modifiable risk factors for development of cardiovascular disease is hypertension(1) . Complications of hypertension account for 9.4 million deaths worldwide every year. Hypertension is res...
Computed Tomography of Normal Adrenal Glands in Indian Population
The aim of our study was to determine the size of normal adrenal glands in Indian population. Measurements of the adrenal glands were obtained from computed tomographic (CT) images in 70 patients , who were undergoing CT...
Heart Failure Admissions in Medical Wards ofa Nigerian Tertiary Hospital.
Introduction: Heart failure is a major clinical problem in the world, and is recognized as a contributor to cardiovascular disease burden in Africa. Previous study on the pattern and prevalence of heart failure among med...
Genetic Risk And Adherence to Healthy Life Style for Prevention of Coronary Artery Disease
Risk factors for coronary artery disease was described in 1930. They are obesity, hypertension, hyperlipidemia, diabetes, smoking, obstructive sleep apnea, insulin resistant, increased C-reactive protein, hyperfibrinogen...