Case Report of a Patient with Situs Inversus Totalis with Ciliary Dysfunction for Laparoscopic Cholecystectomy: Considerations for Safe Peri-Operative Anaesthetic Management
Journal Title: Journal of Medical Science And clinical Research - Year 2017, Vol 5, Issue 12
Abstract
Patients with rare genetic disorders are associated with diverse congenital anomalies and present special challenges to the anaesthesiologist. We report the successful management of a 20 year old female with situs inversus totalis and suspected kartagener syndrome posted for laparoscopic cholecystectomy surgery. Cases of situs inversus with or without ciliary dysfunctions are known to have several structural and functional abnormalities especially those as cardiac, spine and airway malformations, presenting a challenge to an inadequately equipped and mis-informed anaesthesiologist. This calls for an individualisation of the peri-operative concerns of such patients based on associated anomalies along with appropriate monitoring. In this report we highlight the evaluations done and precautions taken during the management of such a patient who underwent successful management at our centre. It is recommended that such patients with multiple congenital anomalies be given a thorough and cautious assessment for a safe intra-operative and postoperative course. Keywords: Peri-operative management. Kartagener syndrome. Situs inversus totalis Key Messages: Cases of situs inversus totalis with ciliary dysfunction reveal a very unique set of problems due to multiple functional and structural abnormalities that might coexist with it. A review of nomenclatures of the abnormalities of left-right asymmetry with specific organ system malformations reported in these patients is presented here and their implications for anaesthetic care are discussed.
Authors and Affiliations
Srabani Basu
Keywords
Related Articles
- EP ID EP521679
- DOI -
- Views 41
- Downloads 0
Sound Pollution effect on Pulse Rate, of Selected Students at the Science and Engineering Workshop
Sound which is a mechanical disturbance that generate waves through an elastic media is characterized by compression and rarefaction, within an audible frequency of 20-20,000Hz. It is a function of industrial and anthrop...
Tubercular Recto-Prostatic Fistula: A Rare Entity
Recto-prostatic fistulas are rare entities in any urology outdoor. Most of the cases reported are by paediatric surgeons dealing with ano-rectal malformations or by surgeons involved in misfortunes of radical prostatecto...
To Study Clinical Profile and Complications of Plasmodium Vivax Malaria
Malaria is caused by Plasmodium parasites. It is a protozoan disease transmitted by the bite of infected Anopheles mosquitoes called "malaria vectors.” Out of the five parasite species that cause malaria in humans, 2 of...
A Prospective study showing incidence of Inguinal Hernia with Undescended Testes in KMC, Katihar
Abstract
Clinical study of Incisional Hernia
Incisional hernia is considered as one of the most common complication after an abdominal surgery postoperatively and an important source of morbidity. This study analyses the various modes of presentation, etiopathogene...