"Cloves Syndrome”-Report of A Rare Case with Lipoma of the Conus As An Additional Feature
Journal Title: IOSR Journal of Dental and Medical Sciences (IOSR-JDMS) - Year 2017, Vol 16, Issue 9
Abstract
CLOVES” stands for Congenital Lipomatous Overgrowth, Vascular malformations, Epidermal naevi, Spinal or Skeletal anomalies. CLOVES Syndrome is extremely rare ,non hereditary, progressive overgrowth disorder, with about 100 cases reported worldwide. The features of this syndrome include truncal lipomatous lesions, cutaneous naevi, vascular anomalies (typically truncal) and spinal anomalies like Scoliosis or skeletal anomalies like limb overgrowth, widened first interdigital space, overgrowth of digits etc. Some are also associated with seizures or central nervous system malformations like hemimegalencephaly. This recent delineation distinguishes it from Proteus syndrome, a disorder that comprises localized, progressive, postnatal overgrowth with bony distortion, dysregulated adipose tissue, cerebriform connective tissue and linear epidermal nevus, hemimegalencephaly, and other manifestations. The author describes the case of a 9 months old child who presented with features of CLOVES syndrome with an additional finding of a lipoma of the conus which has not been reported so far.
Authors and Affiliations
Dr. Shibashish Bhattacharjee
Keywords
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