Contractures of the upper extremities in spinal muscular atrophy type II. Descriptive clinical study with retrospective data collection
Journal Title: Ortopedia Traumatologia Rehabilitacja - Year 2010, Vol 12, Issue 5
Abstract
Introduction: The most significant orthopaedic problem for patients with the intermediate form of spinal muscular atrophy, SMA type II, is the appearance of contractures in addition to progressive scoliosis and pelvic obliquity with increasing loss of sitting stability. This study deals with restrictions of the passive range of motion and the development of contractures in the joints of the upper extremities in these patients. Patients and methods: We followed up 143 patients, 74 female and 69 male, with SMA type II for an average of 5.3 years ( 4.0, 0.2 – 18.7). Their average age at the first examination was 8.4 years ( 6.6, 0.1 – 34.1) and at the last examination 12.3 years ( 6.5, 0.7 – 37.1). The passive range of joint motion was determined using a goniometer. According to Johnson et al. (1992), we calculated the relative contracture index (CI). Results: The loss of range of motion and the contractures of the joints of the upper extremities (shoulder, elbow and wrist) increased progressively with age. The most marked restriction of motion was in the elbow joint with severe flexion contractures in some cases. Conclusion: The findings of this study give us more information about the development of contractures of the upper extremities and aim to help to improve the quality of orthopaedic care of patients with SMA type II.
Authors and Affiliations
Albert Fujak , Carsten Kopschina, Florian Gras, Raimund Forst , Jürgen Forst
Keywords
Related Articles
- EP ID EP57045
- DOI -
- Views 100
- Downloads 0
THE ROLE OF LASER BIOSTIMULATION IN EARLY POST-SURGERY REHABILITATION AND ITS EFFECT ON WOUND HEALING.
Background. The aim of this paper is to investigate whether laser biostimulation starting on the first day after surgery of the brachial plexus or peripheral nerves has a positive therapeutic effect on wound healing. Mat...
Exposure of the Surgeon’s Hands to Radiation During Hand Surgery Procedures
Background. The objective of the study was to assess the time of exposure of the surgeon's hands to radiation and calculate of the equivalent dose absorbed during surgery of hand and wrist fractures with C-arm fluoroscop...
Manual Therapy in the Treatment of Idiopathic Scoliosis. Analysis of Current Knowledge
[b]Background. [/b]Apart from the recommended specific physiotherapy, the treatment of idiopathic scoliosis (IS) also incorporates non-specific manual therapy (NMT). The aim of this paper is to assess the efficacy of NMT...
Patologiczne podkrętarzowe złamanie kości udowej w przebiegu rozległej malformacji tętniczo-żylnej. Studium przypadku
Przedstawiono przypadek 19-letniego mężczyzny z patologicznym podkrętarzowym złamaniem lewej kości udowej w przebiegu rozległej malformacji tętniczo-żylnej lewego uda. Malformację tętniczo-żylną rozpoznano u pacjenta w w...
Złamanie implantu typu OSS jako powikłanie endoprotezoplastyki poresekcyjnej wykonanej z powodu urazu wysokoenergtycznego okolicy stawu kolanowego. Studium przypadku
Zaopatrzenie wysokoenergetycznych złamań części dalszej kości udowej stanowi znaczne wyzwanie. Rozwój metod osteosyntezy umożliwił skuteczne leczenie tego typu złamań, jednak rozległe ubytki kostne powstałe podczas urazu...