Dental and Anaesthetic Challenges in a Patient with Dystrophic Epidermolysis Bullosa

Journal Title: Sultan Qaboos University Medical Journal - Year 2016, Vol 16, Issue 4

Abstract

Epidermolysis bullosa is a group of rare genetic disorders characterised by skin and mucous membrane fragility and systemic manifestations of variable severity. We report a case of dystrophic epidermolysis bullosa in an 18-year-old male patient who presented to the Department of Oral Health at Sultan Qaboos University Hospital, Muscat, Oman, in 2015 with recurrent dental pain and infections. Due to the poor dental status of the patient and anticipated operative difculties due to microstomia and limited mouth opening, the patient underwent full dental clearance under general anaesthesia. Tis article discusses the dental and anaesthetic challenges encountered during the management of this patient and provides a brief literature review.

Authors and Affiliations

Ali Al-Abadi| Departments of Anaesthesia & ICU, Sultan Qaboos University Hospital, Muscat, Oman, Salah A. Al-Azri| Oral & Maxillofacial Surgery Residency Program, Oman Medical Specialty Board, Muscat, Oman, Abdulaziz Bakathir| Departments of Oral Health, Sultan Qaboos University Hospital, Muscat, Oman, Yusra Al-Riyami| Oral & Maxillofacial Surgery Residency Program, Oman Medical Specialty Board, Muscat, Oman

Keywords

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  • EP ID EP14723
  • DOI -
  • Views 315
  • Downloads 16

How To Cite

Ali Al-Abadi, Salah A. Al-Azri, Abdulaziz Bakathir, Yusra Al-Riyami (2016). Dental and Anaesthetic Challenges in a Patient with Dystrophic Epidermolysis Bullosa. Sultan Qaboos University Medical Journal, 16(4), 495-499. https://europub.co.uk/articles/-A-14723