Ectodermal dysplasia: Case report
Journal Title: MedPulse -International Medical Journal - Year 2015, Vol 2, Issue 8
Abstract
Ectodermal dysplasia represents a group of inherited conditions characterized by aplasia or dysplasia of two or more ectodermally derived anatomical structures such as hair, nails, teeth and sweat glands .Two main clinical forms have been described-hypohidrotic and hidrotic type depending upon functioning of sweat gland. Main clinical manifestations include heat intolerance, anodontia or hypodontia, atrichosis or hypotrichosis and dystrophic nails. This is medical illness with psychosocial impact on child and parents. We present two cases one of hypohidrotic type and other of hidrotic type of ectodermal dysplasia. Importance of early prosthetic management has been discussed.
Authors and Affiliations
Nilesh Shewale, Shilpa Shewale
Keywords
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