Extra-Hepatic portal venous obstruction with portal biliopathy in infant presenting as neonatal cholestasis: a rare case report and review of literature
Journal Title: Pediatric Review: International Journal of Pediatric Research - Year 2016, Vol 3, Issue 12
Abstract
Extra-hepatic portal venous obstruction is most common cause of portal hypertension in children. Apart from variceal formation in gastric and esophageal mucosal layer, it has been postulated that external pressure and or ischemic injury play a role in portal biliopathy. We report an unusual case of a 6 month old infant who presented to us with clinical features suggestive of extra-hepatic biliary atresia; diagnosed as EHPVO with portal biliopathy, managed surgically.
Authors and Affiliations
Ajeet Kumar Yadav, Ramkesh Meena, Bhavika YM, Guruayyappa Ramsingh, Vivek Dewan
Keywords
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- EP ID EP227550
- DOI 10.17511
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