Fahr’s Disease: A rare neurodegenerative disorder
Journal Title: Nepal Journal of Neuroscience - Year 2013, Vol 10, Issue 1
Abstract
Fahr’s disease refers to a rare syndrome characterized by symmetrical and bilateral intracranial calcification. While bilateral striopallidodentate calcinosis is commonly referred to as ‘Fahr’s disease’, there are 35 additional names used in the literature for the same condition. Clinically, Parkinsonism or other movement disorders appear to be the most common presentation, followed by cognitive impairment and ataxia. We present a case of striopallidodentate calcinosis presenting with ataxia and fall.
Authors and Affiliations
Dr Gopal Sedain, MS, MCH
Keywords
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