Fetal rhabdomyomatous nephroblastoma -a variant of Wilms tumor: A case report and review of the literature

Journal Title: Pediatric Urology Case Reports - Year 2017, Vol 4, Issue 5

Abstract

Fetal rhabdomyomatous nephroblastoma is a weird variant of Wilms tumor. It’s a chemo-resistant tumor, characterized for invading the collecting system, and having greater rates of bilateral involvement. The tumor chiefly consists of fetal striated muscle with particularly distinct striations and central nuclei, and isolated regions of typical trimorphic nephroblastoma. The following article brings in a new case of this rare pathology, associated with a review of the literature

Authors and Affiliations

Pedraza Bermeo, Adriana Marcela, Ortiz Zableh, Ana Maria, Pérez Niño, Jaime Francisco

Keywords

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  • EP ID EP454476
  • DOI 10.14534/PUCR.2017530420
  • Views 70
  • Downloads 0

How To Cite

Pedraza Bermeo, Adriana Marcela, Ortiz Zableh, Ana Maria, Pérez Niño, Jaime Francisco (2017). Fetal rhabdomyomatous nephroblastoma -a variant of Wilms tumor: A case report and review of the literature. Pediatric Urology Case Reports, 4(5), 364-368. https://europub.co.uk/articles/-A-454476