Haemophagocytic syndrome in an Infant- A rare case report

Journal Title: Scholars Journal of Medical Case Reports - Year 2017, Vol 5, Issue 2

Abstract

Abstract: Hemophagocytic lymphohistiocytosis is a defect in the immune response leading to hypercytokinemia and an unbridled activation of lymphocytes and histiocytes with a uniformly fatal outcome in absence of treatment. We evaluated a 1.5 month old female child, who presented with clinical features of sepsis, but soon developed pancytopenia and deranged coagulation profile. Radiological investigations showed hepatosplenomegaly and bone marrow revealed hemophagocytosis by histiocytes. Keywords: Hemophagocytic lymphohistiocytosis, pancytopenia, fever, bone marrow, infant.

Authors and Affiliations

Dr. Balaji D. Baste, Apoorv Giri, Dr. Ashwin K. Barsagade, Dr. Pradeep S. Umap, Dr. Anuradha V. Shrikhande

Keywords

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  • EP ID EP378913
  • DOI -
  • Views 76
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How To Cite

Dr. Balaji D. Baste, Apoorv Giri, Dr. Ashwin K. Barsagade, Dr. Pradeep S. Umap, Dr. Anuradha V. Shrikhande (2017). Haemophagocytic syndrome in an Infant- A rare case report. Scholars Journal of Medical Case Reports, 5(2), 81-84. https://europub.co.uk/articles/-A-378913