Hereditary Epidermolysis Bullosa (A Two Cases Report)
Journal Title: Scholars Journal of Medical Case Reports - Year 2018, Vol 6, Issue 10
Abstract
Congenital epidermolysis bullosa are rare genodermatoses, clinically characterized by epithelial fragility leading to the formation of bubbles and cutaneous erosions by cleavage between the epidermis and the dermis. We report the observation of two children in care at pediatric plastic surgery department of the Children's Hospital of RABAT for syndactylies involving the fingers of both hands secondary to this pathology and we will focus on the particularity of the management of this rare pathology.
Authors and Affiliations
Rachid Jennine, Driss Hanine, Nawfal Fejjal
Keywords
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