Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report

Journal Title: Journal of Medical and Allied Sciences - Year 2015, Vol 5, Issue 1

Abstract

Heterotaxy syndrome is a rare embryological disorder comprising of polysplenia, partial agenesis of dorsal pancreas, malrotation of gut, cardiac and vascular anomalies resulting from failure of development of the usual left–right asymmetry of organs. We report a rare case of heterotaxy syndrome with polysplenia, partial agenesis of dorsal pancreas and malrotation of gut in a 28 year female presenting with subacute intestinal obstruction along with imaging illustrations, brief discussion and thorough review of literature.

Authors and Affiliations

Syed Althaf Ali| Department of Radiology, Deccan College of Medical Sciences, Kanchanbagh, Hyderabad 500058, Telangana, India, Syeda Naziya P| Department of Anatomy, Deccan College of Medical Sciences, Kanchanbagh, Hyderabad 500058, Telangana, India, Anand Abkari| Department of Radiology, Deccan College of Medical Sciences, Kanchanbagh, Hyderabad 500058, Telangana, India, GSN Murthy| Department of Radiology, Deccan College of Medical Sciences, Kanchanbagh, Hyderabad 500058, Telangana, India, B Ravindra Prakash| Department of Radiology, Deccan College of Medical Sciences, Kanchanbagh, Hyderabad 500058, Telangana, India

Keywords

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  • EP ID EP12721
  • DOI -
  • Views 403
  • Downloads 28

How To Cite

Syed Althaf Ali, Syeda Naziya P, Anand Abkari, GSN Murthy, B Ravindra Prakash (2015). Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report. Journal of Medical and Allied Sciences, 5(1), 10-13. https://europub.co.uk/articles/-A-12721