Hypertrophic cardiomyopathy – symptomatic atrial fibrillation in a patient at high risk of sudden cardiac death
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2019, Vol 4, Issue 1
Abstract
We present the case of a young patient with significant left ventricular hypertrophy as a common representation of the hypertrophic cardiomyopathy (HCM) phenotype. The clinical presentation and diagnostic route of the disease (despite negative genotype), which can be found in everyday cardiology practice, are shown. Despite the presence of guidelines on this topic, each clinical case is demanding, especially during qualification for invasive procedures. Limited data about the periprocedural risk of catheter ablation and success rate in HCM makes physician decisions for this type of patient challenging. The importance of informed consent and how the patient’s decisions affect further progress are also shown. JRCD 2018; 4 (1): 18–21
Authors and Affiliations
Adam Gębka, Renata Rajtar-Salwa, Marek Jastrzębski, Paweł Petkow-Dimitrow
Keywords
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- EP ID EP563421
- DOI 10.2041/jrcd.vol4no1.346
- Views 100
- Downloads 0
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