Isolated Right Subclavian Artery in a Patient with Tetralogy of Fallot with Single Pulmonary Artery

Journal Title: Journal of Cardiovascular Medicine and Surgery - Year 2017, Vol 3, Issue 1

Abstract

Isolated RSCA from the right pulmonary artery is a very rare vascular arch anomaly. Complete loss of continuity of subclavian artery from the aortic arch was named ISOLATION by Stewart and colleagues [4] in 1964. They are commonly associated with DiGeorge syndrome [2] or intracardiac anomalies [3]. We report a case of 6 years old female child diagnosed with Tetralogy of Fallot with single pulmonary (right) artery with no left pulmonary artery with an anomalous Right Subclavian artery arising from the single pulmonary artery with left arch and left superior vena cava. Patient underwent single lung repair with total transatrial approach with reimplantation of the right subclavian artery into the right carotid/ innominate artery (first branch of the ascending aorta). Early intervention with complete surgical repair normalised the patient’s circulation with resolution of both the pulmonary and subclavian steal phenomenon.

Authors and Affiliations

Neeraj Kamat

Keywords

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  • EP ID EP462218
  • DOI 10.21088/jcms.2454.7123.3117.10
  • Views 97
  • Downloads 0

How To Cite

Neeraj Kamat (2017). Isolated Right Subclavian Artery in a Patient with Tetralogy of Fallot with Single Pulmonary Artery. Journal of Cardiovascular Medicine and Surgery, 3(1), 63-66. https://europub.co.uk/articles/-A-462218