Jaffe-Lichtenstein syndrome - Report of a rare case
Journal Title: Journal of Oral Medicine, Oral Surgery, Oral Pathology and Oral Radiology - Year 2018, Vol 4, Issue 4
Abstract
Fibrous dysplasia FD is a benign slow growing skeletal disorder that causes swelling of the bone Lichtenstein described FD in 1938 as skeletal bone disorder which is distinguished by continuous replacement of normal bone with fibrous matrix FD is also associated with JaffeLichtenstein syndrome JLS and McCuneAlbright syndrome MAS JLS is characterized by polyostotic FD along with cafaulait pigmented lesions on the skin MAS presents with additional features of endocrine disorders along with the FD The disease is found to cause significant aesthetic problem and functional disturbance particularly those affecting the craniofacial skeleton Most often the clinical features and the classic radiographic presentation of the pathology would be sufficient to make a diagnosis However other fibroosseous lesions that mimic the radiographic features are critical to make a differential diagnosis for the clinician The present case report is about a 6 year old boy from south India who has been diagnosed as JaffeLichtenstein syndrome JLSKeywords Fibrous dysplasia McCuneAlbright Syndrome Cafeaulaithyperpigmentation LichtensteinJaffes disease Osteitisfibrosa alkaline phosphatase Acid phospatase Bone biopsy
Authors and Affiliations
Shaul Hameed. K, Laxmikant Chatra, Prasanth Shenoy, Anoop Kurian Mathew
Keywords
Related Articles
- EP ID EP479811
- DOI 10.18231/2395-6194.2018.0047
- Views 140
- Downloads 0
Assessment of thickness and echogenic pattern of masseter in subjects with OSMF, chewers and healthy controls- An ultrasound study
Introduction: Oral submucous fibrosis (OSMF), a potentially malignant disorder is associated with prolonged chewing of arecanut which results in fibrosis of the lamina propria. A positive correlation has been observed be...
Role of diode laser in oral submucous fibrosis
Introduction Oral submucous fibrosis is a precancerous condition affecting the oral cavity oropharynx and rarely esophagus tongue and commonly seen in those consuming betel nut Its incidence has been reported 05 of the I...
Lateral Compression Open Cap Splint (MacLennan) - A Treatment Modality for Pediatric Mandibular Parasymphysis Fracture: Case Report
Facial injuries are the most disturbing situations in pediatric patients. The treatment options for the traumatic injuries in pediatric group is controversial as any surgical intervention in young children may disturb th...
“Evaluation and comparison of alveolar bone loss of maxilla and mandible in completely edentulous patients on digital panoramic radiographs”
Aim: Evaluation and comparison of alveolar bone loss of maxilla and mandible in completely edentulous patients on digital panoramic radiographs. Methods: Alveolar bone loss was evaluated on digital panoramic radiograph....
Metastatic Ewing’s Sarcoma of Mandible: A rare case report
Ewing’s Sarcoma (ES) is one of the most aggressive bone tumors which usually occur in children and young adults. The extensive literature search indicates occurrence of only 2-7% cases in the maxillofacial region. Also,...