MULTIPLE KERATOCYSTIC ODONTOGENIC TUMORS: A PRESENTATION OF GORLIN GOLTZ SYNDROME
Journal Title: Journal of Advanced Medical and Dental Sciences Research - Year 2017, Vol 5, Issue 6
Abstract
Background :Gorlin Goltz syndrome is a rare inherited disorder of multiple Keratocystic odontogenic tumors (KCOT) with cutaneous, dento-osseous, ophthalmic, neurological abnormalities. Characteristic findings include multiple KCOTs and basal cell nevi. The KCOT should be treated aggressively due to its recurrence and complications. Method :We discuss two cases of multiple KCOT in young patients, who presented with primary complaints related to the presence of keratocystic odontogenic tumor and were diagnosed as Gorlin Goltz syndrome based on the presence of major and minor diagnostic criteria. Results :Both our cases presented with complaints related to the presence of KCOTs which were treated surgically without evidence of recurrence till date. Conclusions :In Gorlin Goltz syndrome, KCOT’s are often the first clinical feature to be recognised and could be the only condition for which the patient may seek treatment. It is therefore important that OMF surgeons have knowledge of the main features of this syndrome and a high index of suspicion be present when a patient of multiple KCOT presents to our clinics
Authors and Affiliations
Selven Thirumalai, Sumir Gandhi, Inderjot Singh, Navpreet Bedi
Keywords
Related Articles
- EP ID EP557002
- DOI -
- Views 121
- Downloads 0
Analysis of Cases of Anterior Hyperfunction Syndrome: A Clinical Study
Background: Anterior hyperfunction syndrome is when an edentulous maxilla is opposed by natural mandibular anterior teeth. This leads to various complications in patients requiring denture. The present study was conducte...
Comparative Evaluation of Mechanical Properties of Various Elastomeric Impression Materials
Background: During making the impression, the material needs to flow and adhere to the tooth structure and periodontal tissues that may be wetted by blood, saliva, and water. Polyether impression materials are composed o...
Ptosis in Diabetic- Third nerve Palsy or Mucormycosis? A Case Report
Orbital mucormycosis, an opportunistic fungal infection is a rare but life threatening infection that generally occurs in patients with diabetes mellitus and other immune deficiency conditions. As such the condition is a...
A Review on one rare complication “Avascular Necrosis of Maxilla” after Le Fort I Orthognathic Surgery
The sequelae of insufficient vascularity following maxillary orthognathic surgery can vary from loss of tooth vitality, to periodontal defects, to tooth loss to loss of major maxillary dentoalveolar segments. The literat...
Comparison of efficacy of treatment with cyclosporine 0.1% add on therapy with artificial tears (carboxy methyl cellulose 0.5%) & artificial tears alone on dry eye parameters in post cataract surgery patients
Introduction -Cataract is the leading cause of preventable blindness and the only effective treatment is to surgically remove the affected lens and replace it with an artificial lens. Most patients complain of dry eye af...