Multisystem Fibro Inflammatory Disease: A Rare Combination
Journal Title: Journal of Clinical and Diagnostic Research - Year 2018, Vol 12, Issue 2
Abstract
Abstract Idiopathic Retroperitoneal Fibrosis (RPF) is a disease of unknown aetiology, characterised by extensive periaortic sclerosis. A subset of idiopathic RPF is found to be associated with Immunoglobulin G4-Related Disease (IgG4-RD) which is also designated as Multisystem Fibro Inflammatory Disease (MFID). IgG4-RD is an emerging immune mediated disorder of unknown aetiology being increasingly appreciated in recent times. This disorder encompasses a spectrum of disorders involving more than one organ system and shares a common pool of clinical, serological and pathological features. There are few clinical, radiological, pathological and treatment response differences found between the subset of idiopathic RPF that is associated with IgG4-RD and the rest without IgG4-RD association. Here we present a case of MFID with a rare combination of idiopathic RPF causing bilateral ureteral encasement, large bowel obstruction and gross pericardial effusion.
Authors and Affiliations
Sivakami Pradheepkumar
Keywords
Related Articles
- EP ID EP522265
- DOI 10.7860/JCDR/2018/31871.11193
- Views 60
- Downloads 0
Pure Uterine Lipoma: A Common Tumour at an Uncommon Site
Although lipomas are very common tumours, pure uterine lipomas are extremely rare. Their reported incidence is 0.03-0.2%. They commonly present with symptoms similar to that due to leiomyoma except that they occur in pos...
The Effect of Morphine, Codeine and Methadone on Orthodontic Tooth Movement and Histological Features of Bone Tissue in Rats: An Experimental Study
ABSTRACT Introduction: Orthodontic treatments are associated with pain. Opioids are commonly used to alleviate such pain which in turn can interfere with orthodontic treatment. Information about the effect of different t...
Leprosy in Pregnancy: Obstetric Diligence is the Key
Leprosy in pregnancy is a rarely encountered event. Out of the 2000 patients detected of leprosy annually, two to three are pregnant women and majority of them are diagnosed in the third trimester. We, hereby, report a c...
Educational Intervention Based on Protection Motivation Theory to Improve Vitamin E and C Consumption among Iranian Factory Workers
ABSTRACT Introduction: Various studies have suggested the protective role of antioxidant vitamins such as vitamin C and E against toxic injury and disease resulting from toxic metals. Thus, studying the antioxidant vita...
Journey from Fighters to Survivors: Quality of Life and Mental Status in Cancer Patients in a Rural Tertiary Care Hospital
ABSTRACT Introduction: Cancer is a major public health burden in India. Though modern medicine has made tremendous advancements in the treatment of cancers, still morbidity and mortality remain high. It affects different...