KLIPPEL TRENAUNAY SYNDROME: A CASE REPORT
Journal Title: Journal of Evolution of Medical and Dental Sciences - Year 2015, Vol 4, Issue 34
Abstract
[b] INTRODUCTION[/b]: Klippel Trenaunay Syndrome is a rare congenital disorder, but it is the most common condition involving combined vascular malformation. KTS was first described by two French Physicians, Klippel and Trenaunay in 1900.(1)Incidence of KTS reported is approximately 2 to 5 cases per 100, 000 live births.(2,3) KTS generally affects a single extremity, although cases of multiple affected limbs have been reported. The leg is most common site followed by the arms, the trunk, and rarely the head and neck. The original description of KTS included limb hypertrophy, varicose veins and vascular (Port wine) nevus, which were characterised as a clinical triad. Hemangiomatosis is the most frequent finding in these patients and is usually present at birth.(4) KTS is also known as angio -osteohypertrophy syndrome, congenital dysplastic angiopathy or klippel trenaunay weber syndrome.
Authors and Affiliations
Sonali Suman, Ashutosh Sinha, Smita Kumari, Banani Sengupta, Shreemant Gautam
Keywords
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- EP ID EP133043
- DOI 10.14260/jemds/2015/871
- Views 85
- Downloads 0
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