Necrotizing autoimmune myopathy: an emerging entity in the spectrum of inflammatory myopathies
Journal Title: International Journal of Clinical Rheumatology - Year 2018, Vol 13, Issue 2
Abstract
Background: Necrotizing autoimmune myopathy is a relatively newly recognized rare form of idiopathic inflammatory myopathy. It presents clinically with symmetrical proximal muscle pain and weakness, associated with a markedly elevated Creatine kinase level. These myopathies are usually immune mediated with a good response to immunotherapy. Case presentation: We present a case of a 32 year old man of Asian descent, having a 6 months history of symmetrical proximal muscle weakness. Patient underwent extensive workup and was diagnosed with Necrotizing autoimmune myopathy. Conclusion: The disease process of Necrotizing autoimmune myopathy is still not completely understood. However, a delay in the diagnosis may lead to potential complications as the disease progresses rapidly.
Authors and Affiliations
Ishaq M Ghauri, Shariq Mukarram, Noman Khalid
Keywords
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