Newborn with Harlequin Ichthyosis and the Nursing Care
Journal Title: Çocuk Acil ve Çocuk Yoğun Bakım Dergisi - Year 2018, Vol 5, Issue 3
Abstract
Harlequin ichthyosis is the severest form of non-bullous ichthyosis, which is quite uncommon in newborns, and is usually characterized by fatal extreme keratinization of the skin. Because of the facial appearance of newborn, which resembles clown, the disease is called as harlequin -one of the comic characters of Italian street theatre. The present case report concerning a newborn with harlequin ichthyosis, which is an uncommon condition requiring intensive care, aimed to guide the care process by discussing the experiences over the nursing care period. Within the scope of nursing process, the data were collected, the diagnoses were identified, interventions were planned and implemented, and the outcomes of these implementations were evaluated. The nursing diagnoses were made based on the diagnosis list established by the North American Nursing Diagnosis Association. Nursing process was performed within the scope of the activities of daily living. Life expectancy of the patient, who was expected to die within a few days after birth, was extended by efficient and preventive nursing care, but these implementations have not been sufficient to prolong survival. Specific to this case, we can say that death could be postponed by nursing care. Palliative and preventive care is recommended when harlequin ichthyosis is encountered.
Authors and Affiliations
Serap Torun, Handan Demiroğlu
Keywords
Related Articles
- EP ID EP538895
- DOI 10.4274/cayd.78941
- Views 92
- Downloads 0
B-Type Natriuretic Peptide in Bronchiolitis: Its Relationship with Left Ventricular Systolic Functions and Prognosis
Introduction: We have limited information about the clinical importance of plasma B-type natriuretic peptide (BNP) level and its prognostic value in children with bronchiolitis. In this study, we aimed to determine basal...
Retrospective Evaluation of Patients Admitted to the Pediatric Emergency Department with Intoxication
Introduction: In this study, we aimed to retrospectively analyze the demographic and epidemiologic features, clinical course, laboratory results and prognoses of the patients admitted to the department of pediatric emerg...
Evaluation of Patients Diagnosed with Brain Death in Pediatric Critical Care
Introduction: The incidence of brain death in pediatric intensive care units is not known precisely. Studies of brain death-organ donation in children are few and the etiology of brain death in pediatric patients is diff...
Characteristics of Children Admitted to the Emergency Department with Convulsive Epileptic Seizures: A Single-Center Study
Introduction: To evaluate the etiology and characteristics of children admitted to the emergency department with an acute convulsive epileptic seizure. Methods: Data of patients who were admitted to the emergency departm...
Evaluation of the Effects of Serum Starvation and Hypoxic Conditions on Metabolic Pathway Protein Expressions in Breast and Hepatocellular Cancers
Objectives: Adenosine monophosphate (AMP) activating-protein-kinase (AMPK) is a crucial serine/threonine protein kinase that is activated in cellular metabolic stress conditions to maintain cellular energy-homeostasis. U...