OSLER- WEBER -RENDU Disease Presenting As Recurrent Pulmonary Arteriovenous Malformations
Journal Title: IOSR Journal of Dental and Medical Sciences (IOSR-JDMS) - Year 2017, Vol 17, Issue 2
Abstract
Osler-Weber-Rendu Syndrome Is A Rare Genetic Vascular Disorder With Various Clinical Manifestations. Most Common Manifestations Were Epistaxis And Gastrointestinal Bleeding With ArterioVenous (AV) Malformations Also Occurring In Pulmonary And Hepatic Circulation. Management Include Treatment Of Vascular Lesions. Our Case Report Describes A Case Of Hereditary Hemorrhagic Telangiectasia (HHT) Of An Adult Male, Associated With Recurrent A-V Malformations (AVM’s) In Lungs Who Presented With Recurrent epistaxis And hemothorax And Resulting In Breathing Difficulty.He Was Diagnosed With A-V Malformations In Lungs Twice Within 9 Years. On Detailed Evaluation He Was Diagnosedwith Osler‑ Weber‑ Rendu Disease Based OnCuracaocriteria. We Successfully Managed the Patient’s Hemothorax by Thoracentesis. This Case Emphasizes The Need For Careful Examination And Investigation And To Consider Such Rare Diseases When All The Common Causes Of Hemothorax Are Ruled Out.
Authors and Affiliations
Dr Ashwin Yadav1, Dr Dixit Kumar Thakur2
Keywords
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- EP ID EP363350
- DOI 10.9790/0853-1702104648
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