Phakomatosis Pigmentovascularis: Case Report of Type IIa
Journal Title: Dermatology – Open Journal - Year 2016, Vol 1, Issue 1
Abstract
Phakomatosis Pigmentovascularis (PPV) is a rare sporadic developmental disorder characterized by coexistence of a cutaneous vascular malformation and pigmentary nevi. There are different classifications of PPV. When systemic involvement is there, a designation ‘b’ is used, whereas if no systemic involvement, a designation ‘a’ is used. Herein, we reported a 12 years old girl presented with a symptomatic persistent progressive skin lesions since birth.Systemic review and past medical history were all unremarkable. Skin examination revealed mixture of diffuse non-scaly, bleachable erythematous patches, greenish patches, and hypopigmented patches over her trunk. Ophthalmologist and neurologist consulations did not reveal any abnormalities. Based on the above clinical findings, the patient was diagnosed to have port-wine stains, Mongolian spots, and nevus anemicus. Constellation of these clinical findingswithout presence of extracutaneous manifestations made the diagnosis of PPV type IIa.
Authors and Affiliations
Khalid Al Hawsawi
Keywords
Related Articles
- EP ID EP550627
- DOI 10.17140/ DRMTOJ-1-106
- Views 108
- Downloads 0
Analysis of Mortality in a Dermatological Affections Referral Center in Sub-Saharan Africa, Abidjan, République de Côte d'Ivoire
Objectives:To document patients who died in Dermatology Department at University Teaching Hospital (UTH) of Treichville; describe epidemiological aspects; indicate the various dermatological diseases associated; specify...
Erythema Annulare Centrifugum (Deep Type): A Rare Case Report
Erythema annulare centrifugum (EAC) is one of the figurate erythemas. It is uncommon inflammatory condition characterized by annular or arcuate erythematous eruptions that slowly enlarge centrifugally. It persists from f...
Systematic Review of Oral and Topical Botanicals in Reducing Photosensitivity
Objectives: Various treatment options are available for the management of photosensitivity. The objective of this review is to evaluate the use of botanicals rich in antioxidants for photosensitivity reduction.Design: Em...
Emerging Age of Opportunity for More Effective Treatments in Atopic Dermatitis
Atopic dermatitis (AD) is a chronic inflammatory disease characterized by widespread lesions, which manifest as erythematous areas with crusting and/or scaling, oozing, excoriations, and lichenification. Additionally, pr...
Shaping Up Mitochondrion in Motion
We previously reported that hair follicle dermal papilla cells (HFDPCs) show two types of mitochondria, which are filamentous (untangled) and rounded (tangled) mitochondria. Platelet derived growth factor-AA (PDGF-AA) sh...