Pulmonary hypertension inadequate to the clinical condition or hypoxemia disproportionate to the PH severity? (RCD code: II-1B.2)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2015, Vol 2, Issue 5
Abstract
We present four cases of patients with a history of a pulmonary hypertension (PH), who had a component of lung disease disproportionate to the PH severity. Detailed evaluation revealed pulmonary arterial hypertension (PAH) and patients were qualified to the targeted pharmacotherapy, however the treatment did not bring the significant improvement of patients' functional status. During follow-up, we observed deterioration of the clinical symptoms, that were not reflected in a significant progression of the right ventricle dysfunction. This article provides information regarding pathogenesis, clinical characteristics, diagnostic evaluation and treatment of patients with PAH and presents the basic knowledge of the contribution of lung disorders to the PH development. JRCD 2015; 2 (5): 150–155
Authors and Affiliations
Katarzyna Ptaszyńska-Kopczyńska, Remigiusz Kazimierczyk, Małgorzata Jasiewicz, Bożena Sobkowicz, Włodzimierz Musiał, Karol Kamiński
Keywords
Related Articles
- EP ID EP248044
- DOI 10.20418/jrcd.vol2no5.199
- Views 98
- Downloads 0
Adult patient with truncus arteriosus type I. Management and follow‑up (RCD code: IV‑1C.3b)
Truncus arteriosus is a congenital heart malformation where systemic, pulmonary and coronary circulation is supplied by a single artery arising from the heart. Surgical correction of this disorder remains the treatment...
4th Symposium on Rare Cardiovascular Diseases – ESC Barcelona 2014
Raport from the Satellite Symposium on Rare Cardiovascular Diseases.
Female patient after correction of tetralogy of Fallot with severe pulmonary regurgitation and significant left-to-right shunt at the ventricular septal level (RCD code: IV-5A2)
Tetralogy of Fallot (ToF) is the most common cyanotic congenital heart disease after 1 year of age. Less than 5% of all patients with uncorrected ToF live beyond the age of 40 years. Prognosis after surgical correction i...
World Rare Disease Day – 29th of February 2016 III Conference of Rare Cardiovascular Diseases at John Paul II Hospital in Krakow
The third Conference of Rare Cardiovascular Diseases took place at the John Paul II Hospital in Krakow, Poland on the 29th of February 2016. The conference was organized as part of the World Rare Disease Day 2016 annuall...
Health‑related quality of life in pulmonary arterial hypertension (RCD code: II)
Health-related QoL (HRQoL) is defined as ‘‘the functional effect of an illness and its consequent therapy upon a patient, as perceived by the patient’’ and is a reflection of one’s health on physical, psychological, and...