Pulmonary hypertension inadequate to the clinical condition or hypoxemia disproportionate to the PH severity? (RCD code: II-1B.2)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2015, Vol 2, Issue 5
Abstract
We present four cases of patients with a history of a pulmonary hypertension (PH), who had a component of lung disease disproportionate to the PH severity. Detailed evaluation revealed pulmonary arterial hypertension (PAH) and patients were qualified to the targeted pharmacotherapy, however the treatment did not bring the significant improvement of patients' functional status. During follow-up, we observed deterioration of the clinical symptoms, that were not reflected in a significant progression of the right ventricle dysfunction. This article provides information regarding pathogenesis, clinical characteristics, diagnostic evaluation and treatment of patients with PAH and presents the basic knowledge of the contribution of lung disorders to the PH development. JRCD 2015; 2 (5): 150–155
Authors and Affiliations
Katarzyna Ptaszyńska-Kopczyńska, Remigiusz Kazimierczyk, Małgorzata Jasiewicz, Bożena Sobkowicz, Włodzimierz Musiał, Karol Kamiński
Keywords
Related Articles
- EP ID EP248044
- DOI 10.20418/jrcd.vol2no5.199
- Views 87
- Downloads 0
“A rare day to put rare diseases in the spotlight!” “With research possibilities are limitless”
Just few days ago, on 28th February, the tenth edition of Rare Disease Day was launched by EURORDIS and its Council for National Alliances to attract thousands people all over the world to come together to advocate for m...
Transradial carotid artery stenting with the use of a novel integrated embolic protection technology
We present the case of a 79‑year‑old woman with critical right internal carotid artery stenosis in whom carotid artery stenting was performed via a right radial artery approach with the use of a novel integrated embolic...
Long QT syndrome diagnosed in the postpartum period (RCD code: VII-V-1A.2)
We report a case of 22 years old woman with long QT syndrome type with the first cardiac incidents in the post partum period. We discuss the actual treatment recommendation in the long QT syndrome with special attention...
1st Conference for Adults with Congenital Heart Diseases. “Care for congenital heart disease patients in Poland”
The population of adults with congenital heart disease (ACHD) is heterogeneous with respect to the type and complexity of the defect as well as its clinical manifestations. In many patients congenital heart disease (CHD)...
Pregnancy in patient with Turner syndrome, after surgery for coarctation of the aorta, with bicuspid aortic valve and ascending aortic aneurysm (RCD code: VII-I-1B.6)
A 30‑year‑old woman with Turner Syndrome was admitted to our centre in 12th week of her first pregnancy with a history o surgical correction of coarctation of aorta. She was asymptomatic with good general condition. Tran...