Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
Journal Title: Sultan Qaboos University Medical Journal - Year 2018, Vol 18, Issue 2
Abstract
Dermatofibrosarcomas protuberans (DFSP) are rare low-grade tumours with various subtypes and usually occur among middle-aged adults. However, myoid differentiation is very rare. We report a 44-year-old woman who presented to the Lok Nayak Jai Prakash Hospital, New Delhi, India, in 2017 with a recurrent pigmented DFSP presenting as an arm swelling. Upon histological and immunohistochemical analysis, myoid differentiation was confirmed. A literature review of the clinical and histopathological features of this rare entity is presented.
Authors and Affiliations
Surekha Yadav, Nidhi Verma, Nita Khurana, Sushant Neogi
Keywords
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- EP ID EP34703
- DOI http://dx.doi.org/10.18295/squmj.2018.18.02.019
- Views 342
- Downloads 0
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