Retroperitoneal Paraganglioma in Children (About a Rare Case)
Journal Title: Scholars Journal of Medical Case Reports - Year 2018, Vol 6, Issue 10
Abstract
Retroperitoneal paragangliomas are rare tumors. They are defined as extra-adrenal chromaffin tumors and represent approximately 1 / 5th of chromaffin tumors. They are often asymptomatic and can reach important dimensions. We report the case of a 7-year-old boy operated on for a giant retroperitoneal tumor whose pathological examination concluded that he had a paraganglioma. The malignant forms, more frequent than the benign forms, present a locoregional invasion and metastasize late. Management of paragangliomas should be multidisciplinary but only surgical treatment is curative. On the other hand, there is no consensus on the usefulness of complementary therapies, which may nonetheless be supportive as a symptom. Paragangliomas are genetic in 25% of cases. A genetic survey must be systematically proposed.
Authors and Affiliations
Driss Hanine, Meryam Ramzi, Zakaria Aboulam, Rachid Oulahyane, Mounir Kisra
Keywords
Related Articles
- EP ID EP489539
- DOI -
- Views 73
- Downloads 0
Ranula Arising From Sublingual Gland
Oral ranula is a retention cyst arising from the sublingual gland on the floor of the mouth as a result of ductal obstruction and fluid retention1. Management of ranula becomes controversial. Various surgical options hav...
A Case in which a Patient Intoxicated by Synthetic Cannabinoids was Diagnosed by a Mass Spectrometry Analysis
Abstract: A 20-year-old man who was accompanied by another man who was sitting in the passenger seat, bumped into a guardrail while driving a car at low speed. When the emergency medical technician checked them, the pas...
A Case of Bullous LE with Secondary Nephrotic Syndrome
Abstract: Lupus erythematosus (LE) of the skin comprises an uncommon group of skin disorders, most often affecting young adult women (aged 20 to 50), but children, elderly and males may also be affected. Here we report a...
A Case of Gastric Emphysema Accidentally Found By Computed Tomography for the Evaluation of Trauma
Abstract:The patient was a 55-year-old man who had fallen from a height of 1.5 m when cutting a tree branch. He complained of face, chest, back, right femur and leg pain. He had hypertension and gastritis. He was diagno...
A case of essential thrombocythemia complicated with spontaneous chest wall hematoma
Abstract:A 66-year-old female noticed right thoracic back pain when she woke up in the morning in 5 days. This gradually deteriorated and called an ambulance. She did not have any episode of trauma. She had a history of...