Retroperitoneal Paraganglioma in Children (About a Rare Case)
Journal Title: Scholars Journal of Medical Case Reports - Year 2018, Vol 6, Issue 10
Abstract
Retroperitoneal paragangliomas are rare tumors. They are defined as extra-adrenal chromaffin tumors and represent approximately 1 / 5th of chromaffin tumors. They are often asymptomatic and can reach important dimensions. We report the case of a 7-year-old boy operated on for a giant retroperitoneal tumor whose pathological examination concluded that he had a paraganglioma. The malignant forms, more frequent than the benign forms, present a locoregional invasion and metastasize late. Management of paragangliomas should be multidisciplinary but only surgical treatment is curative. On the other hand, there is no consensus on the usefulness of complementary therapies, which may nonetheless be supportive as a symptom. Paragangliomas are genetic in 25% of cases. A genetic survey must be systematically proposed.
Authors and Affiliations
Driss Hanine, Meryam Ramzi, Zakaria Aboulam, Rachid Oulahyane, Mounir Kisra
Keywords
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