Rzadki przypadek złośliwego nerwiaka osłonkowego jamy nosa

Journal Title: Polski Przegląd Otorynolaryngologiczny - Year 2014, Vol 3, Issue 4

Abstract

Malignant peripheral nerve sheath tumors (MPNSTs) are sarcomas which originate from peripheral nerves or from cells associated with the nerve sheath. MPNSTs comprise approximately 5–10% of all soft tissue sarcomas. They can occur either spontaneously or in association with neurofibromatosis-1 (NF1). They are usually deep-seated and often involve the proximal upper and lower extremities as well as the trunk. Because MPNSTs can arise from multiple cell types, the overall appearance can vary greatly from one case to the next. This can make diagnosis and classification somewhat difficult. The mainstay of treatment is surgical resection. Most of these tumors are considered high-grade sarcomas with the potential to recur as well as to metastasize. We present a very rare case a woman 51-years-old with malignant peripheral nerve sheath tumor localized in right nasal cavity.

Authors and Affiliations

Agata Pala-Sadza, Hanna Zajączkiewicz, Renata Banaś-Samson, Iwona Glinianowicz, Jolanta Ożóg, Ewa Gnacik-Stawarczyk, Martyna Dubrawska, Beniamin Rauch

Keywords

Related Articles

Salvage surgery of hypopharyngeal cancer as a second malignancy post radiotherapy and the possibility of digestive track reconstruction – study of three cases and the literature review

Patients with head and neck cancers have an increased risk of second malignant neoplasm occurrence (25% in long-term follow-up, 4% yearly). Most patients with a primary tumor can be treated with organ-preserving strategi...

Początki historii zastosowania lasera CO2 w chirurgii krtani w Polsce

Chirurgia laserowa CO2 w krtani jest związana z prof. Gezą Juliusem Jako, który jako pierwszy w 1972 r. opisał kliniczne wyniki zastosowania lasera CO2 u chorych. W Polsce po raz pierwszy 28 kwietnia 1983 r., w Katedrze...

Venous malformation of epiglottis and arterio-venous malformation of palate treated by sclerotherapy – case reports

This study presents two rare clinical entities of vascular anomalies localized in the region of head and neck: the case of woman with venous malformation of the epiglottis and the man with the arterio-venous malformation...

Edmund Kuncewicz (1906–1962), man of merit for otorhinolaryngology in Ostrów Wielkopolski

Edmund Kuncewicz (1906–1962) was well-known specialist in otorhinolaryngology, born in Vilnius. His achievements during the second world war and his doctor's activity in Vilnius after this war is mentioned. Edmund Kuncew...

Download PDF file
  • EP ID EP51278
  • DOI -
  • Views 182
  • Downloads 0

How To Cite

Agata Pala-Sadza, Hanna Zajączkiewicz, Renata Banaś-Samson, Iwona Glinianowicz, Jolanta Ożóg, Ewa Gnacik-Stawarczyk, Martyna Dubrawska, Beniamin Rauch (2014). Rzadki przypadek złośliwego nerwiaka osłonkowego jamy nosa. Polski Przegląd Otorynolaryngologiczny, 3(4), -. https://europub.co.uk/articles/-A-51278