Senning operation as a palliative therapy for a girl with complex heart defect and Eisenmenger syndrome (RCD code: II‑1A.4d)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2016, Vol 3, Issue 1
Abstract
Development of irreversible pulmonary hypertension in D-transposition of the great arteries (D-TGA) with ventricular septal defect (VSD) is a well-known phenomenon. Coexistence of left ventricular outflow tract obstruction (LVOTO) should theoretically protect the patient against pulmonary arterial hypertension (PAH). Application of the Blalock-Taussig shunt (B-TS) temporarily improves condition of the patient, but may contribute to irreversible PAH requiring palliative complex therapy. We present a case of a 18 year-old female with congenital complex heart defect: D-TGA with inflow VSD and subpulmonary stenosis, Eisenmenger syndrome, who was treated with several subsequent palliative cardiosurgical operations, including B-TS and Senning procedure and eventually, combined PAH-specific therapy, what resulted in stabilization of clinical status. JRCD 2016; 3 (1): 14–16
Authors and Affiliations
Jacek Kuźma, Andrzej Rudziński, Grzegorz Kopeć, Piotr Weryński, Dorota Palczewska, Daniel Porada, Marek Rączka, Maciej Pitak
Keywords
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- EP ID EP244134
- DOI 10.20418/jrcd.vol3no1.236
- Views 89
- Downloads 0
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