Soft Tissue Rosai-Dorfman Disease Case report
Journal Title: Sultan Qaboos University Medical Journal - Year 2017, Vol 17, Issue 4
Abstract
Rosai-Dorfman disease (RDD) is a rare benign proliferative histiocytic disorder characterised by massive lymphadenopathy. While extranodal involvement can occur in generalised RDD, isolated soft tissue RDD (STRDD) is extremely rare. We report a 17-year-old male patient who presented to the maxillofacial outpatient department of the Sultan Qaboos Hospital, Salalah, Oman, in 2015 with a painless cheek mass which had been slowly growing over the previous two months. Routine histopathological examinations and immunohistochemistry confrmed a diagnosis of STRDD. Currently, surgical excision is considered to be the most effective curative treatment for STRDD, as the outcomes of other treatment modalities are still unknown. Despite its rarity, STRDD should be considered in the differential diagnosis of histiocytic soft tissue lesions.
Authors and Affiliations
Rubyath C. Rajib| Department of Pathology & Laboratory Medicine, Sultan Qaboos Hospital, Salalah, Oman, Rajasekharan Pillai| Department of Pathology & Laboratory Medicine, Sultan Qaboos Hospital, Salalah, Oman, Ibrahim A. Sulaiman| Department of Pathology & Laboratory Medicine, Sultan Qaboos Hospital, Salalah, Oman, Ibrahim Al-Haddabi| Department of Pathology, College of Medicine & Health Sciences, Sultan Qaboos University, Muscat, Oman
Keywords
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- EP ID EP14823
- DOI 10.18295/squmj.2017.17.04.012
- Views 384
- Downloads 24
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