Thoracoscopic management of recurrent spontaneous pneumothorax and incidentally detected eventration of diaphragm in a case of Marfan’s syndrome: A case report
Journal Title: Scholars Journal of Medical Case Reports - Year 2016, Vol 4, Issue 4
Abstract
Recurrent pneumothorax has been reported in patients with Marfan syndrome and is more common in such patients. We report a case of a child who had 2 episodes of spontaneous pneumothorax. Patient was treated by intercostal drainage tube on each episode. After 2nd episode, patient was investigated by CT thorax. No evidence of bullae/emphysema was found. After 3 weeks he again presented with 3rd episode of spontaneous pneumothorax. Thoracoscopy was done, no bullous/emphysematous lesion found, incidental finding of eventration of left dome of diaphragm was found which was corrected by plication. Pleurodesis was done on post-op day 5 to prevent recurrence of spontaneous pneumothorax. Patient had uneventful recovery and was discharged and is on regular follow-up.This case is rare as association of Marfan syndrome with eventration of diaphragm has not been reported in pediatric patient while recurrent spontaneous pneumothorax is a known complication in this syndrome. Keywords: Marfan syndrome, pneumothorax, Thoracoscopy, eventration, Pleurodesis
Authors and Affiliations
Dr. Patil Prashant S, Dr. Gupta Abhaya, Dr. Kothari Paras L, Dr. Kekre Geeta, Dr. Kamble Ravi, Dr. Dikshit Vishesh K
Keywords
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