Visual Impairment in Orbitofrontal and Sphenoidal Fibrous Dysplasia Associated with Sphenoid Sinus Mucocele
Journal Title: Journal of Clinical Research and Ophthalmology - Year 2015, Vol 2, Issue 4
Abstract
The orbitofrontal fibrous dysplasia is a rare, non-malignant disease that involves the development and thickening of craniofacial bones, causing facial asymmetry, visual, neurological and dental complications. Decreased visual acuity in orbitofrontal and sphenoidal fibrous dysplasia appears as a result of compressive lesions on the optic nerve. The aim of this article is to present the ophthalmologic complications due to the association of two entities that both involved the optic nerve: orbitofrontal fibrous dysplasia associated with a large sphenoid sinus mucocele. We report the case of a 20-years old male patient, who was admitted to the Neurosurgery Unit II of “Prof. Dr. Nicolae Oblu” Emergency Clinical Hospital, Iassy, Romania, for headache, sudden decrease in visual acuity of both eyes in the last month, though more markedly in his right eye and facial deformity with right frontal bony bulging. The patient hadn’t in his previous medical history any dermatological or endocrinological diseases. The ophthalmologic examination revealed that the visual acuity of the right eye was hand movements and best corrected visual acuity of the left eye was 20/60. Conventional X-ray, CT and MRI investigations showed an orbitofrontal and sphenoidal fibrous dysplasia associated with a large sphenoid sinus mucocele, located in the anterior and middle cranial fossa. Two surgical procedures were performed, the first being an attempt to perform a bilateral decompression of the optic nerve and in the second one, was evacuated the large sphenoid sinus mucocele, that compressed the optic chiasm. The first histopathological examination confirmed that the orbitofrontal and sphenoidal lesion had a typical appearance of fibrous dysplasia and the second biopsy revealed a sphenoid sinus mucocele. Six months after the evacuation of the sphenoid sinus mucocele, patient recovered completely his vision only in the left eye (20/20) and the right eye had no light perception, he also developed a peripheral right facial nerve palsy.
Authors and Affiliations
Claudia Florida Costea, Andrei Cucu, Victor Vlad Costan, Gabriela Florența Dumitrescu, Anca Sava, Dana Mihaela Turliuc
Keywords
Related Articles
- EP ID EP230956
- DOI 10.17352/2455-1414.000022
- Views 92
- Downloads 0
Cutaneous Horn of the Eyelid: Anatomoclinical Implications
Cutaneous horns are relatively rare benign tumors which occur most frequently on sun exposed skin and develop on various types of underlying skin lesions: benign, premalignant and malignant. The treatment of choice consi...
The “Crocodile Technique”: A New Ophthalmic Surgical Technique to Remove Subretinal Proliferative Tissue Associated with Retinal Detachment
Purpose: To describe the “crocodile technique”, a new ophthalmic surgery technique for removing subretinal proliferative tissue (SPT) associated with retinal detachment.
Long-Term Outcome of Approved Pharmacotherapy for Diabetic Macular Edema: A Review of Randomized Controlled Trials in Fluocinolone Acetonide Implants, Dexamethasone Implants, Aflibercept and Ranibizumab
Diabetic macular edema (DME) is a major sight-threatening cause in diabetic patients. The pathophysiology of macular edema involves both the presence of inflammation and angiogenic stimulant regarding vascular endothelia...
Bilateral iris, lens and Chorioretinal Coloboma: A Case Report
Colobomas are genetic malformations due to lack of closure of the embryonic fissure. These are rare malformations that can sit at any level of the eye. Colobomas can be uni or bilateral, sporadic or hereditary. It may be...
Bilateral Numerous Warts in Upper and Lower Eyelids, in Middle-Aged Man
Background: Warts are small, usually painless growths on the skin caused by a virus called human papillomavirus (HPV). Most, but not all, are generally harmless [1,2]. Warts can be disfiguring and embarrassing. Sometime...