Von Willebrand disease - broadening our vision: a pediatric case report with dental considerations
Journal Title: Journal of Dental Specialities - Year 2017, Vol 5, Issue 1
Abstract
Von Willebrand disease is an autosomal inherited bleeding disorder caused due to the quantitative or qualitative defects of a multimeric glycoprotein, the Von Willebrand factor (VWF). VWF is a multi-adhesive protein that carries factor VIII in circulation and initiates aggregation of platelets to exposed sub endothelial collagen fibers. The deficiency or abnormality of VWF causes reduction in the levels of factor VIII, as seen in Hemophilia A patients. The common clinical manifestations of Von Willebrand disease include soft tissue and mucosal bleeding. The severity of the disease is determined by the extent of von Willebrand factor and factor VIII reduction in the circulation. Since symptoms are often mild, a significant majority of patients remain undiagnosed. This article presents the ongoing dental management of a seven-year old female diagnosed with Von Willebrand disease. The primary aim of the article is to focus on the diagnosis, management and dental considerations of this common yet overlooked disorder and distinguish it from Hemophilia.
Authors and Affiliations
Mridula Goswami, Deepti Thakkar
Keywords
Related Articles
- EP ID EP298594
- DOI -
- Views 63
- Downloads 0
Awareness towards management and prevention of dental injuries among sports instructors in Delhi, India
Background/Aim: The purpose of this study was to assess the level of awareness towards management and prevention of dental injuries among sports instructors in Delhi, India, by a self-administered questionnaire. Material...
Conservative management of parotid fistula and sialocele
Sialocele is a collection of saliva in the subcutaneous tissue or in the glandular tissues. When this communicates with the skin and drains it is known as parotid fistula. The causes are sharp penetrating trauma, infecti...
Antibiotic prescription patterns in a Dental college located in Northern India
Introduction: Antibiotics are a boon for infection control; however, injudicious prescription of these drugs cause resistance and is a matter of concern. The assessment of awareness and knowledge of antibiotics prescript...
Effect of educational status on oral health education program amongst Anganwadi workers in improving oral health of preschool children of Muradnagar block, Ghaziabad-A cross-sectional study
Aim To study effect of educational status of Anganwadi Workers on oral health education program and its impact on improving oral health of preschool children in Muradnagar block GhaziabadMaterials and Methods Study was d...
Use of a semi-precision attachment to fabricate a removable partial denture – a case report
Use of attachments in providing better retention to removable prosthesis is not an outdated treatment modality. It is important for dentists to have more updated knowledge about its use and the success of such prosthesis...