31-year old man with Short QT syndrome (RCD code: V-1A.3)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2016, Vol 2, Issue 7
Abstract
Short QT (SQTS) syndrome is a rare inherited autosomal dominant cardiac channelopathy associated with malignant ventricular and atrial arrhythmias. It is the severest form of the major channelopathies, with cardiac arrest or sudden cardiac death (SCD) as the most common presentation. We report a case of a young patient in whom ventricular fibrillation was the first manifestation of the disease.
Authors and Affiliations
Sylwia Wiśniowska-Śmiałek, Paweł Rubiś, Katarzyna Holcman, Barbara Biernacka-Fijałkowska, Agata Leśniak-Sobelga, Magdalena Kostkiewicz, Piotr Podolec, Grzegorz Kopeć
Keywords
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- EP ID EP245351
- DOI 10.20418/jrcd.vol2no7.220
- Views 89
- Downloads 0
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