31-year old man with Short QT syndrome (RCD code: V-1A.3)

Journal Title: Journal of Rare Cardiovascular Diseases - Year 2016, Vol 2, Issue 7

Abstract

Short QT (SQTS) syndrome is a rare inherited autosomal dominant cardiac channelopathy associated with malignant ventricular and atrial arrhythmias. It is the severest form of the major channelopathies, with cardiac arrest or sudden cardiac death (SCD) as the most common presentation. We report a case of a young patient in whom ventricular fibrillation was the first manifestation of the disease.

Authors and Affiliations

Sylwia Wiśniowska-Śmiałek, Paweł Rubiś, Katarzyna Holcman, Barbara Biernacka-Fijałkowska, Agata Leśniak-Sobelga, Magdalena Kostkiewicz, Piotr Podolec, Grzegorz Kopeć

Keywords

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  • EP ID EP245351
  • DOI 10.20418/jrcd.vol2no7.220
  • Views 102
  • Downloads 0

How To Cite

Sylwia Wiśniowska-Śmiałek, Paweł Rubiś, Katarzyna Holcman, Barbara Biernacka-Fijałkowska, Agata Leśniak-Sobelga, Magdalena Kostkiewicz, Piotr Podolec, Grzegorz Kopeć (2016). 31-year old man with Short QT syndrome (RCD code: V-1A.3). Journal of Rare Cardiovascular Diseases, 2(7), 228-230. https://europub.co.uk/articles/-A-245351