45‑year‑old man with hypertrophic cardiomyopathy after alcohol ablation, progression to dilated cardiomyopathy (RCD code: III‑1B.8a)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2014, Vol 2, Issue 1
Abstract
Hypertrophic cardiomyopathy (HCM) is the most common inheritable cardiac disorder with an estimated prevalence of 1:500 in the general population. In minority of patients, with the prevalence approximately of 3–5%, HCM progresses into dilated, end-stage or burn-out phase, characterized by LV wall thinning, systolic dysfunction and LV cavity dilatation. We present a case of a 45 year-old man with endstage HCM with postcapillary pulmonary hypertension, who was experimentally treated with sildenafil. It resulted in noticeable clinical and haemodynamical improvement. JRCD 2014; 2 (1): 23–26
Authors and Affiliations
Sylwia Wiśniowska-Śmiałek, Paweł Rubiś, Barbara Biernacka-Fijałkowska, Marcin Kunecki, Marta Hlawaty, Agata Leśniak-Sobelga, Magdalena Kostkiewicz, Piotr Podolec
Keywords
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- EP ID EP245450
- DOI 10.20418/jrcd.vol2no1.157
- Views 111
- Downloads 0
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