A rare case report of anaesthetic management in a paediatric patient with Christ-Siemens-Touraine syndrome

Abstract

Ectodermal dysplasia (ED) is a heterogeneous group of disorders which may involve teeth, skin and appendageal structures including hairs, nails, eccrine and sebaceous glands. As ED is very rare in occurrence, the available literature is scarce. We are describing a case of 3 year old male child with suspected foreign body (nose) posted for emergency nasal endoscopy. Anticipating difficult airway, frequent pulmonary infections, temperature monitoring are important considerations in anaesthesia management in a case of patient with Ectodermal Dysplasia. Thorough knowledge about Ectodermal Dysplasia is important to an Anaesthesiologist to tackle related complications in emergency scenarios.

Authors and Affiliations

Sonali Khobragade, Leena I ngle, Amol Jatale, Jitendra Bhagat

Keywords

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  • EP ID EP494219
  • DOI -
  • Views 78
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How To Cite

Sonali Khobragade, Leena I ngle, Amol Jatale, Jitendra Bhagat (2017). A rare case report of anaesthetic management in a paediatric patient with Christ-Siemens-Touraine syndrome. INTERNATIONAL JOURNAL OF RECENT TRENDS IN SCIENCE AND TECHNOLOGY, 22(1), 60-62. https://europub.co.uk/articles/-A-494219