A unique collection of Rombergs disease- A rare clinical entity
Journal Title: Medpulse International Journal of Pathology - Year 2018, Vol 8, Issue 1
Abstract
Background: Parry Romberg Syndrome (progressive facial hemiatrophy) is characterized by slowly progressive atrophy of subcutaneous tissue. Bones, muscles, nerves, eyes and brain may be affected by atrophy of unknown origin. This condition was first described by Romberg and Parry in 1846.Eulenberg named the disorder in the year 1872.The aim of this study is to discuss in detail the series of these cases with this rare entity at our institute and their treatment options. Methods: This is a retrospective and prospectivestudy conducted in patients treated in Plastic Surgery department at Asram Hospital. Results: Out of 9 patients studied, 5 (55.5%) were females and 4(44.4%) were males. The youngest age of the patient affected was 12 years and oldest was 34 years. The left hemiface was most commonly affected. Seven(77%) patients underwent surgery. Conclusions: Romberg’s syndrome is an extremely rare disease with threatening complications. Extensive studies on stem cells have been made to treat this disease. However, its etiopathogenesis is still unconquered.
Authors and Affiliations
K Anji Reddy, Vahini G
Keywords
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- EP ID EP457132
- DOI 10.26611/105813
- Views 100
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