Bamboo Hair Syndrome or Netherton Syndrome - A Case Report
Journal Title: IOSR Journal of Dental and Medical Sciences (IOSR-JDMS) - Year 2017, Vol 16, Issue 3
Abstract
Netherton Syndrome (AKA- Bamboo Hair Syndrome) is a non treatable, Autosomal Recessive Disorder of infancy and childhood, so has no sex predilection. Family history may reveal consanguinity. There is triad - A] Ichthyosiform linearis circumflexa B] Hair Shaft Defect like trichorrhexis invaginata & C] Atopic Diathesis.
Authors and Affiliations
Puja Balpande
Keywords
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- DOI 10.9790/0853-1603106769.
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